Morquio Syndrome for Aortic Valve Replacement: Anesthesia Concerns - A Case Report.
J, T., S, V., M, M., KP, U., & VT, P. (2026). Morquio Syndrome for Aortic Valve Replacement: Anesthesia Concerns - A Case Report.. Annals of cardiac anaesthesia. https://doi.org/10.4103/aca.aca_249_25
J T, S V, M M, KP U, VT P. Morquio Syndrome for Aortic Valve Replacement: Anesthesia Concerns - A Case Report.. Annals of cardiac anaesthesia. 2026; doi: 10.4103/aca.aca_249_25
J T, S V, M M, et al. Morquio Syndrome for Aortic Valve Replacement: Anesthesia Concerns - A Case Report.[J]. Annals of cardiac anaesthesia. 2026. DOI: 10.4103/aca.aca_249_25.
@article{j2026,
author = {Talukdar J and Vondutla S and Munaf M and Unnikrishnan KP and Panicker VT},
title = {Morquio Syndrome for Aortic Valve Replacement: Anesthesia Concerns - A Case Report.},
journal = {Annals of cardiac anaesthesia},
year = {2026},
doi = {10.4103/aca.aca_249_25},
note = {PMID: 42441778},
}
TY - JOUR AU - Talukdar J AU - Vondutla S AU - Munaf M AU - Unnikrishnan KP AU - Panicker VT TI - Morquio Syndrome for Aortic Valve Replacement: Anesthesia Concerns - A Case Report. T2 - Annals of cardiac anaesthesia PY - 2026 DO - 10.4103/aca.aca_249_25 AN - PMID:42441778 ER -
Morquio syndrome is a lysosomal storage disease that can lead to glycosaminoglycan deposition in the tissues. Skeletal deformities, cardiovascular complications, and airway abnormalities are well-recognized in this condition, specifically owing to thickened mucosa and epiglottis, making fiberoptic-guided intubation less successful. Our patient had severe aortic regurgitation and was posted for aortic valve replacement. Anesthetic challenges encountered during the management of the case, and a different approach to airway management are highlighted in this report. With increased survival of patients affected with Morquio syndrome, cardiac anesthesiologists might see an increasing number of similar patients requiring corrective cardiac surgery.